Macroglossia

Macroglossia, a big tongue, is a rare condition mostly related to specific syndromes. The most common syndrome associated with macroglossia is Beckwith-Wiedemann syndrome, and it is sometimes associated with trisomy 21. Macroglossia can be best visualized on the facial profile view. The coronal view is also helpful. A nomogram for tongue measurement has been established.

Fig 1

The major causes of macroglossia are as follows:

  • Beckwith-Wiedemann syndrome
  • Athyrotic hypothyroidism
  • Trisomy 21, 22
  • Autosomal dominant macroglossia
  • Harlequin fetus (congenital ichthyosis)
  • Mass of the tongue; lingual thyroid, lingual hemangioma, lymphangioma
  • Epignathus.

 

Fig 1: Macroglossia   Facial profile view: persistent protruding tongue (arrow) (in fetal Down syndrome)

Video clips of facial clefts

Macroglossia: Midsagittal facial profile shows persistent protrusion of the enlarged tongue